Repeated local Recurrence of Dermatofibrosarcoma Protuberans in the Anterior Chest Wall of a Child
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Abstract
Dermatofibrosarcoma protuberans (DFSP) is a very rare, low-intermediate-grade sarcoma of the dermis layer of the skin; it has a marked propensity for local recurrence after excision. It is typically diagnosed during early adult life at a tumoral stage and it occurs rarely in children. This report is a case of childhood DFSP that had recurred five times within a period of eight years, each following surgical excision. This tumor also showed an uncommon myxoid change: Appearing as larger multi-nodular cutaneous plaque that arose at the site of excision of previous tumors some years earlier. The rarity of this tumor, and the fact that it is even rarer in children, prompted the report of this case.
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References
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